Congenital factor II deficiency

What is Congenital factor II deficiency?

An inherited bleeding disorder due to reduced activity of factor II (FII, prothrombin) and characterized by mucocutaneous bleeding symptoms.

Other condition names

  • Dysprothrombinemia
  • Hypoprothrombinemia
  • Prothrombin deficiency

Inheritance type

Autosomal recessive

Prevalence

  • Europe: <1 in 1,000 000

Age of Onset

  • All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.