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Congenital factor VII deficiency
What is Congenital factor VII deficiency?
A rare, genetic, congenital vitamin K-dependant coagulation factor deficiency disorder characterized by decreased levels or absence of coagulation factor VII (FVII), resulting in bleeding diathesis of variable severity.
Other condition names
Congenital proconvertin deficiency
Hypoproconvertinemia
Inheritance type
Autosomal dominant, Autosomal recessive
Prevalence
Europe: 1-9 in 1,000 000
Age of Onset
All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.