Congenital factor VII deficiency
What is Congenital factor VII deficiency?
A rare, genetic, congenital vitamin K-dependant coagulation factor deficiency disorder characterized by decreased levels or absence of coagulation factor VII (FVII), resulting in bleeding diathesis of variable severity.
Other condition names
- Congenital proconvertin deficiency
- Hypoproconvertinemia
Inheritance type
Autosomal dominant, Autosomal recessive
Prevalence
- Europe: 1-9 in 1,000 000
Age of Onset
- All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.