Congenital factor VII deficiency

What is Congenital factor VII deficiency?

A rare, genetic, congenital vitamin K-dependant coagulation factor deficiency disorder characterized by decreased levels or absence of coagulation factor VII (FVII), resulting in bleeding diathesis of variable severity.

Other condition names

  • Congenital proconvertin deficiency
  • Hypoproconvertinemia

Inheritance type

Autosomal dominant, Autosomal recessive


  • Europe: 1-9 in 1,000 000

Age of Onset

  • All ages
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