Cushing syndrome due to macronodular adrenal hyperplasia
What is Cushing syndrome due to macronodular adrenal hyperplasia?
A rare cause of Cushing syndrome (CS) characterized by nodular enlargement of both adrenal glands (multiple nodules above 1 cm in diameter) that produce excess cortisol and features of adrenocorticotropic hormone (ACTH) independent CS.
Other condition names
- Primary bilateral macronodular adrenal hyperplasia
Inheritance type
Autosomal dominant, Not applicable
Prevalence
- Europe: <1 in 1,000 000
Age of Onset
- All ages
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