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Cushing syndrome due to macronodular adrenal hyperplasia

What is Cushing syndrome due to macronodular adrenal hyperplasia?

A rare adrenal Cushing syndrome characterized by bilateral benign adrenal macronodules (>1 cm) that potentially produce autonomously variable levels of cortisol excess. Although in most cases are ACTH-independent, non-suppressed ACTH levels have been described.

Other condition names

  • Primary bilateral macronodular adrenal hyperplasia

Inheritance type

Autosomal dominant, Not applicable

Prevalence

  • Europe: <1 in 1,000 000

Age of Onset

  • All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.