Dentin dysplasia-sclerotic bones syndrome

What is Dentin dysplasia-sclerotic bones syndrome?

Dentin dysplasia-sclerotic bones syndrome is a rare, genetic odontologic disease characterized by the clinical, radiographic, and histologic features of dentine dysplasia and osteosclerosis of all long bones, with heavy cortical bone and narrowed or occluded marrow spaces. There have been no further descriptions in the literature since 1977.


  • Worldwide: <1 in 1,000 000

Age of Onset

  • Infancy
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