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Dubin-Johnson syndrome

What is Dubin-Johnson syndrome?

Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterized clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.

Other condition names

  • Dubin-Sprinz disease
  • Hyperbilirubinemia type 2
  • Sprinz-Nelson syndrome

Inheritance type

Autosomal recessive

Age of Onset

  • Adolescent
  • Adult
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.