Early myoclonic encephalopathy

What is Early myoclonic encephalopathy?

A rare disorder characterized clinically by the onset of fragmentary myoclonus appearing in the first month of life, often associated with erratic focal seizures and a suppression-burst EEG pattern.

Other condition names

  • Early myoclonic encephalopathy with suppression-bursts

Inheritance type

Autosomal dominant, Autosomal recessive


  • Worldwide: <1 in 1,000 000

Age of Onset

  • Infancy
  • Neonatal
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