Skip to Accessibility Menu Skip to Login Skip to Content Skip to Footer

Early-onset cerebellar ataxia with retained tendon reflexes

What is Early-onset cerebellar ataxia with retained tendon reflexes?

Early onset cerebellar ataxia with retained reflexes (EOCARR) or Harding ataxia is a cerebellar ataxia characterized by the progressive association of a cerebellar and pyramidal syndrome with progressive cerebellar ataxia, brisk tendon reflexes, and sometimes profound sensory loss.

Other condition names

  • EOCA
  • EOCARR
  • Harding ataxia

Inheritance type

Autosomal recessive

Prevalence

  • Europe: 1-9 in 100,000

Age of Onset

  • Adolescent
  • Adult
  • Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.