Ectopic aldosterone-producing tumor

What is Ectopic aldosterone-producing tumor?

Ectopic aldosterone-producing tumor is an extremely rare aldosterone-producing neoplasm composed of aberrant adrenocortical tissue located outside the adrenal glands (e.g. in retroperitoneum, perirenal or periaortic fatty tissue, thorax, spinal canal, testes, ovaries) typically characterized by symptoms related to increased aldosterone levels (such as sustained, treatment-resistant hypertension and hypokalemia) or symptoms caused by local tumor enlargement.

Other condition names

  • Extra-adrenal aldosterone-producing tumor

Inheritance type

Not applicable

Age of Onset

  • All ages
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