Eosinophilic fasciitis

What is Eosinophilic fasciitis?

Eosinophilic fasciitis is a rare connective tissue disease that is characterized by inflammation and thickening of the fascia, usually associated with peripheral eosinophilia. It presents during adulthood with symmetrical and painful swelling of mainly the extremities that progressively become indurated. Fatigue, disabling cutaneous fibrosis, myositis and arthritis may also be observed.

Other condition names

  • Diffuse fasciitis with eosinophilia
  • Shulman syndrome

Inheritance type

Unknown

Prevalence

  • Worldwide: Unknown

Age of Onset

  • Adult
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