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Eosinophilic granulomatosis with polyangiitis
What is Eosinophilic granulomatosis with polyangiitis?
A rare systemic vasculitis of small vessels characterized by asthma, blood and tissue eosinophilia and vasculitis manifestations.
Other condition names
Churg-Strauss syndrome
EGPA
Granulomatous allergic angiitis
Inheritance type
Not applicable
Prevalence
Europe: 1-9 in 100,000
Worldwide: 1-9 in 100,000
Age of Onset
Adolescent
Adult
Elderly
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.