Eosinophilic granulomatosis with polyangiitis

What is Eosinophilic granulomatosis with polyangiitis?

Eosinophilic granulomatosis with polyangiitis (EGPA), previously known as Churg-Strauss syndrome, is a systemic vasculitis of small-to medium vessels, characterized by asthma, transient pulmonary infiltrates, and hypereosinophilia.

Other condition names

  • Churg-Strauss syndrome
  • EGPA
  • Granulomatous allergic angiitis

Inheritance type

Not applicable


  • Europe: 1-9 in 100,000
  • Worldwide: 1-9 in 100,000

Age of Onset

  • Adolescent
  • Adult
  • Elderly
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.