Evans syndrome

What is Evans syndrome?

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Other condition names

  • Autoimmune hemolytic anemia and autoimmune thrombocytopenia
  • Immune pancytopenia

Inheritance type

Not applicable

Prevalence

  • Europe: 1-9 in 1,000 000

Age of Onset

  • Adult
  • Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.