Familial calcium pyrophosphate deposition

What is Familial calcium pyrophosphate deposition?

A rare inherited rheumatologic disease which causes calcification of articular fibrocartilage or hyaline cartilage, a process termed chondrocalcinosis (CC). It often associates with acute synovitis and osteoarthritis (OA).

Other condition names

  • Calcium pyrophosphate dihydrate crystal deposition disease
  • Familial CC
  • Familial CPPD
  • Familial articular chondrocalcinosis
  • Hereditary CC
  • Hereditary articular chondrocalcinosis
  • Hereditary calcium pyrophosphate deposition

Inheritance type

Autosomal dominant, Not applicable

Age of Onset

  • Adult
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