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Familial hemophagocytic lymphohistiocytosis

What is Familial hemophagocytic lymphohistiocytosis?

Familial Hemophagocytic lymphohistiocytosis (FHL) is a rare primary immunodeficiency characterized by a macrophage activation syndrome (see this term) with an onset usually occurring within a few months or less common several years after birth.

Other condition names

  • Familial HLH

Inheritance type

Autosomal recessive

Age of Onset

  • Adolescent
  • Infancy
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.