Familial progressive cardiac conduction defect

What is Familial progressive cardiac conduction defect?

A genetic cardiac rhythm disease that may progress to complete atrioventricular (AV) block. The disease is either asymptomatic or manifests as dyspnea, dizziness, syncope, abdominal pain, heart failure or sudden death.

Other condition names

  • Familial Lenègre disease
  • Familial Lev disease
  • Familial Lev-Lenègre disease
  • Familial PCCD
  • Familial progressive heart block
  • Hereditary bundle branch defect

Inheritance type

Autosomal dominant


  • Worldwide: Unknown

Age of Onset

  • Adult
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.