Febrile infection-related epilepsy syndrome
What is Febrile infection-related epilepsy syndrome?
Febrile infection-related epilepsy syndrome (FIRES) describes an explosive-onset, potentially fatal acute epileptic encephalopathy that develops in previously healthy children and adolescents following the onset of a non-specific febrile illness.
Other condition names
- AERRPS
- Acute encephalitis with refractory repetitive partial seizures
- Acute non-herpetic encephalitis with severe refractory status epilepticus
- DESC syndrome
- Devastating epileptic encephalopathy in school-aged children
- FIRES
- Fever-induced refractory epileptic encephalopathy in school-aged children
- Idiopathic catastrophic epileptic encephalopathy
- Severe refractory status epilepticus owing to presumed encephalitis
Inheritance type
Not applicable
Age of Onset
- All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.