Fibrous dysplasia of bone

What is Fibrous dysplasia of bone?

A rare, benign, primary bone dysplasia characterized by progressive replacement of normal bone and marrow with fibrous connective tissue in either one (monostotic) or multiple (polyostotic) bones. Clinical manifestations depend on the anatomic location of the replacement and may include bone pain, deformities, pathological fractures, and cranial nerve deficits.

Inheritance type

Not applicable

Age of Onset

  • Adolescent
  • Adult
  • Childhood
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