Hereditary cerebral hemorrhage with amyloidosis

What is Hereditary cerebral hemorrhage with amyloidosis?

A rare genetic cerebral small vessel disease characterized by amyloid deposition in the cerebral blood vessels leading to predominantly hemorrhagic strokes, focal neurological deficits, and progressive cognitive decline eventually leading to dementia.

Other condition names

  • HCHWA

Inheritance type

Autosomal dominant

Prevalence

  • Worldwide: <1 in 1,000 000

Age of Onset

  • Adult
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