Infantile digital fibromatosis

What is Infantile digital fibromatosis?

Infantile digital fibromatosis is a rare, benign, superficial fibromatosis characterized by firm, pinkish to flesh-colored, solitary or multiple nodular growths, typically less than 2 cm in size. They occur on the dorsal or lateral aspect of fingers and toes and have a tendency to recur. Histology reveals bland intradermal spindle cells with spherical perinuclear inclusion bodies.

Other condition names

  • Inclusion body fibromatosis
  • Recurring digital fibrous tumor of childhood
  • Reye tumor

Prevalence

  • Worldwide: <1 in 1,000 000

Age of Onset

  • Childhood
  • Infancy
  • Neonatal
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