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Left ventricular noncompaction
What is Left ventricular noncompaction?
A rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.
Other condition names
LVNC
Left ventricular hypertrabeculation
Spongy myocardium
Inheritance type
Autosomal dominant, Autosomal recessive, Mitochondrial inheritance, X-linked recessive
Age of Onset
All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.