Left ventricular noncompaction
What is Left ventricular noncompaction?
A rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.
Other condition names
- LVNC
- Left ventricular hypertrabeculation
- Spongy myocardium
Inheritance type
Autosomal dominant, Autosomal recessive, Mitochondrial inheritance, X-linked recessive
Age of Onset
- All ages
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