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Left ventricular noncompaction

What is Left ventricular noncompaction?

Left ventricular noncompaction (LVNC) is a rare cardiomyopathy characterized anatomically by prominent left ventricular trabeculae and deep intratrabecular recesses causing progressive systolic and diastolic dysfunction, conduction abnormalities, and occasionally thromboembolic events.

Other condition names

  • LVNC
  • Left ventricular hypertrabeculation
  • Spongy myocardium

Inheritance type

Autosomal dominant, Autosomal recessive, Mitochondrial inheritance, X-linked recessive

Age of Onset

  • All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.