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Mucopolysaccharidosis type 6
What is Mucopolysaccharidosis type 6?
Mucopolysaccharidosis type 6 (MPS 6) is a lysosomal storage disease with progressive multisystem involvement, associated with a deficiency of arylsulfatase B (ASB) leading to the accumulation of dermatan sulfate.
Other condition names
ARSB deficiency
ASB deficiency
Arylsulfatase B deficiency
MPS6
MPSVI
Maroteaux-Lamy disease
Mucopolysaccharidosis type VI
N-acetylgalactosamine 4-sulfatase deficiency
Inheritance type
Autosomal recessive
Prevalence
Europe: 1-9 in 1,000 000
Age of Onset
Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.