Mucous membrane pemphigoid

What is Mucous membrane pemphigoid?

A rare autoimmune bullous skin disease characterized clinically by blistering of the mucous membranes followed by scarring, and immunologically characterized by IgG, IgA and/or C3 deposits on the epidermal basement membrane. The disease principally involves the oral mucosa, but may also affect ocular, pharyngolaryngeal, genital, and esophageal mucous membranes.

Other condition names

  • Cicatricial pemphigoid
  • Mucosal pemphigoid
  • Mucosynechial pemphigoid

Inheritance type

Not applicable

Age of Onset

  • Adolescent
  • Adult
  • Childhood
  • Elderly
  • Infancy
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