Myoclonus-dystonia syndrome

What is Myoclonus-dystonia syndrome?

Myoclonus-dystonia syndrome (MDS) is a rare movement disorder characterized by mild to moderate dystonia along with 'lightning-like' myoclonic jerks.

Other condition names

  • Alcohol-responsive dystonia
  • Hereditary essential myoclonus
  • Myoclonic dystonia

Inheritance type

Autosomal dominant, Not applicable

Prevalence

  • Europe: 1-9 in 1,000 000

Age of Onset

  • Adolescent
  • Adult
  • Childhood
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