Paraneoplastic pemphigus

What is Paraneoplastic pemphigus?

A rare form of autoimmune bullous skin disease characterized by polyformative skin lesions, typically beginning on the oral mucus membranes, and generally associated with lymphoma or chronic lymphoid leukemia.

Inheritance type

Not applicable


  • Worldwide: <1 in 1,000 000

Age of Onset

  • All ages
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