Pemphigus vulgaris

What is Pemphigus vulgaris?

A rare autoimmune bullous skin diseases characterized by painful, flaccid blisters and erosions of the oral mucosa, predominantly involving the buccal area, and with or without extension to the epidermis. Mucosa of the larynx, oesophagus, conjunctiva, nose, genitalia and anus, are less frequently affected.

Inheritance type

Not applicable


  • Europe: 1-5 in 10,000

Age of Onset

  • Adult
  • Childhood
  • Elderly
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "". Data version 1.3.16 / 4.1.7.