Tell us about your symptoms and treatment experience. Take our survey here.

Persistent left superior vena cava connecting through coronary sinus to left-sided atrium

What is Persistent left superior vena cava connecting through coronary sinus to left-sided atrium?

Persistent left superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by a persitent left superior vena cava which drains directly to the left atrium, without passing through the coronary sinus (that may be absent in some cases). Patients are usually asymptomatic and discovered incidentally, however hypoxia, cyanosis, murmurs, palpitations, cardiac structural anomalies (e.g. atrial septal defect, bicuspid aortic valve, cor triatrium) and risk of paradoxical embolization may be associated.

Other condition names

  • Persistent left SVC connecting through coronary sinus to left-sided atrium
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.