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Primary biliary cholangitis
What is Primary biliary cholangitis?
Primary biliary cholangitis (PBC) is a chronic and slowly progressive cholestatic liver disease of autoimmune etiology characterized by injury of the intrahepatic bile ducts that may eventually lead to liver failure.
Other condition names
Hanot syndrome
PBC
Primary biliary cirrhosis
Inheritance type
Multigenic/multifactorial, Unknown
Prevalence
Worldwide: 1-5 in 10,000
Europe: 1-5 in 10,000
United States: 1-5 in 10,000
Age of Onset
Adolescent
Adult
Elderly
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.