Primary oculocerebral lymphoma

What is Primary oculocerebral lymphoma?

Primary oculocerebral lymphoma is a rare, primary, organ-specific, extranodal non-Hodgkin's lymphoma (typically diffuse large B-cell lymphoma), simultaneously affecting the intraocular compartments (retina, vitreous, optic nerve, uvea and others) and the central nervous system (commonly the cerebellum, spinal cord or pia mater). The presenting symptoms vary depending on the localization of the tumor and may include vitreous floaters or blurred vision, raised intracranial pressure (headache, vomiting, papilledema) and/or focal neurological deficits.

Other condition names

  • Primary oculocerebral non-Hodgkin lymphoma

Inheritance type

Not applicable

Age of Onset

  • Adult
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