Proximal renal tubular acidosis

What is Proximal renal tubular acidosis?

Proximal renal tubular acidosis (pRTA) is a tubular kidney disease characterized by impaired ability of the proximal tubule to reabsorb bicarbonate from the glomerular filtrate leading to hyperchloremic metabolic acidosis.

Other condition names

  • Renal tubular acidosis type 2
  • pRTA

Inheritance type

Autosomal dominant, Autosomal recessive, Not applicable


  • Worldwide: Unknown

Age of Onset

  • All ages
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