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Recessive dystrophic epidermolysis bullosa inversa
What is Recessive dystrophic epidermolysis bullosa inversa?
A rare subtype of dystrophic epidermolysis bullosa (DEB) characterized by blisters and erosions which from adolescence or early adulthood are primarily confined to flexural skin sites.
Other condition names
Dystrophic epidermolysis bullosa inversa
Inverse RDEB
Inverse recessive dystrophic epidermolysis bullosa
RDEB-I
Inheritance type
Autosomal recessive
Prevalence
Worldwide: <1 in 1,000 000
Age of Onset
Infancy
Neonatal
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.