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Right superior vena cava connecting to left-sided atrium
What is Right superior vena cava connecting to left-sided atrium?
Right superior vena cava connecting to the left-sided atrium is a rare, congenital vascular malformation of the major vessels characterized by the right SVC passing medially and dorsally to the aortic root and draining into the left atrium. Patients usually present a right-to-left systemic venous blood shunt which may manifest with arterial hypoxemia, cyanosis, exercise dyspnea, clubbing of the fingers, palpitations, murmurs and/or potentially fatal brain abscess. Association with other cardiac anomalies has been reported.
Other condition names
Right SVC connecting to left-sided atrium
Right superior caval vein connecting to left-sided atrium