Severe early-childhood-onset retinal dystrophy

What is Severe early-childhood-onset retinal dystrophy?

Severe early childhood onset retinal dystrophy (SECORD) is an inherited retinal dystrophy characterized by a severe congenital night blindness, progressive retinal dystrophy and nystagmus. Best corrected visual acuity can reach 0.3 in the first decade of life and can pertain well into the second decade of life. Blindness is often complete by the age of 30 years.

Other condition names

  • Early-onset severe retinal dystrophy

Inheritance type

Autosomal recessive


  • Worldwide: Unknown

Age of Onset

  • Childhood
  • Infancy
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "". Data version 1.3.16 / 4.1.7.