Sorsby pseudoinflammatory fundus dystrophy

What is Sorsby pseudoinflammatory fundus dystrophy?

Sorsby's fundus dystrophy is a rare progressive autosomal dominant macular dystrophy, presenting between the third and sixth decades of life, characterized by retinal atrophy and retinal detachment and leading to loss of central vision, then peripheral vision, and eventually blindness.

Inheritance type

Autosomal dominant

Age of Onset

  • Adult
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