Sporadic Creutzfeldt-Jakob disease

What is Sporadic Creutzfeldt-Jakob disease?

A subacute fatal neurodegenerative disease belonging to the group of prion diseases, characterized by a clinical triad of dementia, myoclonus, and EEG anomalies, along with neuropathological evidence of neuronal loss, spongiform changes, and astrocytosis. There are three types of CJD: sporadicCJD (sCJD), inherited CJD , and iatrogenic and variant CJD (vCJD).

Other condition names

  • Sporadic CJD

Inheritance type

Not applicable


  • United States: <1 in 1,000 000
  • Worldwide: <1 in 1,000 000

Age of Onset

  • Adult
  • Elderly
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