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Tietz syndrome
What is Tietz syndrome?
Tietz syndrome is a genetic hypopigmentation and deafness syndrome characterized by congenital profound bilateral sensorineural hearing loss and generalized albino-like hypopigmentation of skin, eyes and hair.
Other condition names
Hypopigmentation-deafness syndrome
Hypopigmentation-hearing loss syndrome
Inheritance type
Autosomal dominant
Prevalence
Worldwide: <1 in 1,000 000
Age of Onset
Neonatal
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.