White sponge nevus

What is White sponge nevus?

White sponge nevus (WSN) is a rare and autosomal dominant genetic disease in which the oral mucosa is white or greyish, thickened, folded, and spongy. The onset is early in life, and both sexes are affected equally. Other common sites include the tongue, floor of the mouth, and alveolar mucosa.

Other condition names

  • Hereditary mucosal leukokeratosis
  • White sponge nevus of Cannon

Inheritance type

Autosomal dominant

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