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Wolfram syndrome
What is Wolfram syndrome?
A rare, genetic, endocrine disorder characterized by type I diabetes mellitus (DM), diabetes insipidus (DI), sensorineural deafness (D), bilateral optical atrophy (OA) and neurological signs.
Other condition names
DIDMOAD syndrome
Diabetes insipidus-diabetes mellitus-optic atrophy-deafness syndrome
Diabetes insipidus-diabetes mellitus-optic atrophy-hearing loss syndrome
Inheritance type
Autosomal recessive
Prevalence
Worldwide: 1-9 in 1,000 000
Europe: 1-9 in 1,000 000
Age of Onset
Adolescent
Adult
Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.