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Hereditary Amyloidosis

What is Hereditary Amyloidosis?

A group of rare kidney diseases known for amyloid fibril deposition of apolipoprotein A-I or A-II (AApoAI or AApoAII amyloidosis), lysozyme (ALys amyloidosis) or fibrinogen A-alpha chain (AFib amyloidosis) in one or several organs. Leads to chronic kidney disease. Kidney failure is a common sign. Other symptoms depend on the organ involved and the type of amyloid fibrils deposited.

Other condition names

  • Amyloidosis, Ostertag type
  • Familial amyloid nephropathy
  • Familial renal amyloidosis
  • Hereditary amyloid nephropathy
  • Hereditary renal amyloidosis

Inheritance type

Autosomal dominant

Age of Onset

  • All ages

Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.