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Wild Type ATTR Amyloidosis
What is Wild Type ATTR Amyloidosis?
A common form of systemic amyloidosis characterized by deposition of wild type transthyretin predominantly in the heart and the soft tissues (mainly the carpal tunnel region, lumbar canal and tendons).
Other condition names
ATTRwt amyloidosis
ATTRwt-related amyloidosis
SSA
Senile systemic amyloidosis
Wild type ATTR-related amyloidosis
Inheritance type
Not applicable
Prevalence
Worldwide: 1-5 in 10,000
Age of Onset
Adult
Elderly
How is amyloidosis treated?
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.