Atypical hemolytic uremic syndrome

What is Atypical hemolytic uremic syndrome?

A rare thrombotic microangiopathy disorder characterized by mechanical hemolytic anemia, thrombocytopenia, and renal dysfunction.

Other condition names

  • Atypical HUS
  • aHUS

Inheritance type

Autosomal dominant, Autosomal recessive, Not applicable


  • Europe: 1-9 in 100,000

Age of Onset

  • All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "". Data version 1.3.16 / 4.1.7.