Atypical hemolytic uremic syndrome
What is Atypical hemolytic uremic syndrome?
A rare, genetic thrombotic microangiopathy due to dysregulation of the alternative complement pathway and characterized by the triad of hemolytic anemia, thrombocytopenia, and acute renal dysfunction.
Other condition names
- Atypical HUS
- aHUS
Inheritance type
Autosomal dominant, Autosomal recessive, Not applicable
Prevalence
- Europe: 1-9 in 100,000
Age of Onset
- All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.