Budd-Chiari syndrome

What is Budd-Chiari syndrome?

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Inheritance type

Multigenic/multifactorial

Prevalence

  • Europe: 1-9 in 100,000
  • Worldwide: 1-9 in 100,000

Age of Onset

  • All ages
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.