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Dentinogenesis imperfecta

What is Dentinogenesis imperfecta?

Dentinogenesis imperfecta (DGI) is a hereditary dentin defect (see this term) characterized by abnormal dentin structure resulting in abnormal tooth development.

Other condition names

  • DGI
  • DGI without OI
  • DI
  • Dentinogenesis imperfecta without osteogenesis imperfecta
  • Non-syndromic DGI
  • Non-syndromic dentinogenesis imperfecta
  • Opalescent teeth without OI
  • Opalescent teeth without osteogenesis imperfecta

Inheritance type

Autosomal dominant

Prevalence

  • Europe: 1-5 in 10,000

Age of Onset

  • Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.