Granulomatosis with polyangiitis
What is Granulomatosis with polyangiitis?
A rare anti-neutrophil cytoplasmic antibodies (ANCA)-associated vasculitis characterized by necrotizing inflammation of small and medium vessels (capillaries, venules and arterioles), resulting in tissue ischemia.
Other condition names
- GPA
Inheritance type
Not applicable
Prevalence
- Europe: 1-9 in 100,000
- United States: 1-9 in 100,000
Age of Onset
- Adolescent
- Adult
- Childhood
- Elderly
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.