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Granulomatosis with polyangiitis
What is Granulomatosis with polyangiitis?
A rare anti-neutrophil cytoplasmic antibodies (ANCA)-associated vasculitis characterized by necrotizing inflammation of small and medium vessels (capillaries, venules and arterioles), resulting in tissue ischemia.
Other condition names
GPA
Inheritance type
Not applicable
Prevalence
Europe: 1-9 in 100,000
United States: 1-9 in 100,000
Age of Onset
Adolescent
Adult
Childhood
Elderly
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.