Idiopathic achalasia

What is Idiopathic achalasia?

Idiopathic achalasia (IA) is a primary esophageal motor disorder characterized by loss of esophageal peristalsis and insufficient lower esophageal sphincter (LES) relaxation in response to deglutition.

Other condition names

  • Achalasia cardia
  • Idiopathic achalasia of esophagus
  • Primary achalasia

Inheritance type

Autosomal recessive, Not applicable


  • Worldwide: 1-9 in 100,000

Age of Onset

  • All ages
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