Lhermitte-Duclos disease

What is Lhermitte-Duclos disease?

A very rare disorder characterized by abnormal development and enlargement of the cerebellum, and an increased intracranial pressure.

Other condition names

  • Dysplastic gangliocytoma of the cerebellum
  • LDD

Inheritance type

Autosomal dominant, Not applicable


  • Worldwide: <1 in 1,000 000

Age of Onset

  • Adult
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