What is Nephroblastoma?

A rare malignant renal tumor, typically affecting the pediatric population, characterized by an abnormal proliferation of cells that resemble the kidney cells of an embryo (metanephroma), leading to the term embryonal tumor.

Other condition names

  • Renal embryonic tumor
  • Wilms tumor

Inheritance type

Autosomal dominant, Not applicable


  • Europe: 1-9 in 100,000

Age of Onset

  • Childhood
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "". Data version 1.3.16 / 4.1.7.