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PAGOD syndrome
What is PAGOD syndrome?
PAGOD syndrome is a severe developmental syndrome characterized by multiple congenital anomalies including cardiovascular defects, pulmonary hypoplasia, diaphragmatic defects and genital anomalies.
Other condition names
Pulmonary hypoplasia-agonadism-dextrocardia-diaphragmatic hernia syndrome
Inheritance type
Not applicable
Prevalence
Worldwide: <1 in 1,000 000
Age of Onset
Neonatal
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.