Segmental odontomaxillary dysplasia

What is Segmental odontomaxillary dysplasia?

Segmental odontomaxillary dysplasia (SOD) is a rare disorder characterized by unilateral enlargement of the right or left maxillary alveolar bone and gingiva in the region from the back of the canines to the maxillary tuberosity. In the enlarged region, dental abnormalities such as missing teeth, abnormal spacing and delayed eruption occur.

Inheritance type

Not applicable


  • Worldwide: <1 in 1,000 000

Age of Onset

  • Childhood
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