Wild type ABeta2M amyloidosis
What is Wild type ABeta2M amyloidosis?
A form of amyloidosis affecting patients with chronic kidney disease (CKD), on long term dialysis characterized by the accumulation of amyloid fibrils consisting of beta 2 microglobulin (β2M) deposits in the musculoskeletal system leading to carpal tunnel syndrome (CTS), chronic arthropathy, cystic bone lesions, destructive osteoarthropathy, and pathologic fractures.
Other condition names
- ABeta2Mwt amyloidosis
- Dialysis-related amyloidosis
- Dialysis-related arthropathy
- Wild type ABeta2-microglobulinic amyloidosis
Inheritance type
Not applicable
Prevalence
- Europe: 1-9 in 100,000
Age of Onset
- Adult
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on "https://www.orphadata.com". Data version 1.3.16 / 4.1.7.