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Acute intermittent porphyria
What is Acute intermittent porphyria?
A form of acute hepatic porphyria characterized by the occurrence of neurovisceral attacks without cutaneous symptoms.
Inheritance type
Autosomal dominant
Prevalence
Europe: 1-9 in 1,000 000
Age of Onset
Adolescent
Adult
Orphadata: Free access data from Orphanet. © INSERM 1999. Available on
"https://www.orphadata.com"
. Data version 1.3.16 / 4.1.7.