Epidermal nevus syndrome

What is Epidermal nevus syndrome?

Epidermal nevus syndrome (ENS) is a rare congenitally acquired syndrome, characterized by the presence of epidermal nevi in association with various developmental abnormalities of the skin, eyes, nervous, skeletal, cardiovascular and urogenital systems.

Other condition names

  • Epidermal hamartoma syndrome

Inheritance type

Not applicable


  • Worldwide: Unknown

Age of Onset

  • Infancy
  • Neonatal
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